Novel Pediatric Aggressive Adipose Tumor With Pathogenic TERT Promoter Variant and an Initial Durable Response to Vincristine and Dactinomycin.

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Title: Novel Pediatric Aggressive Adipose Tumor With Pathogenic TERT Promoter Variant and an Initial Durable Response to Vincristine and Dactinomycin.
Authors: Hare L; Department of Cancer and Genomic Sciences, University of Birmingham, Birmingham, UK.; Department of Paediatric Oncology, Birmingham Children's Hospital, Birmingham, UK., Hughes J; Department of Radiology, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK., Morgan M; Department of Radiology, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK., Burke GAA; Department of Paediatric Oncology, Birmingham Children's Hospital, Birmingham, UK.; Cancer Research UK Clinical Trials Unit, University of Birmingham, Birmingham, UK., Trotman J; East Genomic Laboratory Hub (GLH) Genetics Laboratory, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK., Tarpey P; East Genomic Laboratory Hub (GLH) Genetics Laboratory, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK., Hatcher H; Department of Oncology, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK., Ford SJ; Department of Cancer and Genomic Sciences, University of Birmingham, Birmingham, UK.; Midlands Abdominal and Retroperitoneal Sarcoma Unit, University Hospitals Birmingham NHS Foundation Trust, Birmingham, UK., Watkins AJ; East Genomic Laboratory Hub (GLH) Genetics Laboratory, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.; Department of Histopathology, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK., Hook CE; Department of Histopathology, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.; Department of Pathology, University of Cambridge, Cambridge, UK., Murray MJ; Department of Pathology, University of Cambridge, Cambridge, UK.; Department of Paediatric Haematology and Oncology, Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Source: Pediatric blood & cancer [Pediatr Blood Cancer] 2026 May; Vol. 73 (5), pp. e70193. Date of Electronic Publication: 2026 Mar 15.
Publication Type: Letter
Journal Info: Publisher: John Wiley Country of Publication: United States NLM ID: 101186624 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1545-5017 (Electronic) Linking ISSN: 15455009 NLM ISO Abbreviation: Pediatr Blood Cancer Subsets: MEDLINE; In Process
Database: MEDLINE Ultimate
Description
ISSN:1545-5017
DOI:10.1002/1545-5017.70193