Effects of Elexacaftor/Tezacaftor/Ivacaftor on cough frequency, physical activity patterns, and sleep quality in adolescents and adults with cystic fibrosis.

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Title: Effects of Elexacaftor/Tezacaftor/Ivacaftor on cough frequency, physical activity patterns, and sleep quality in adolescents and adults with cystic fibrosis.
Authors: Van Braeckel E; Department of Respiratory Medicine, Ghent University Hospital, Ghent, Belgium; Department of Internal Medicine and Paediatrics, Faculty of Medicine and Health Sciences, Ghent University, Ghent, Belgium. Electronic address: Eva.VanBraeckel@UGent.be., Braun AT; University of Wisconsin School of Medicine and Public Health, Madison, WI, USA., Simmonds NJ; National Heart and Lung Institute, Imperial College London UK, Royal Brompton Hospital, part of Guy's and St Thomas' NHS Foundation Trust, London, UK., Barry PJ; Manchester University NHS Foundation Trust, Manchester, UK; Division of Infection, Immunity and Respiratory Medicine, University of Manchester, Manchester, UK., Davies JC; National Heart and Lung Institute, Imperial College London UK, Royal Brompton Hospital, part of Guy's and St Thomas' NHS Foundation Trust, London, UK., Egan ME; Yale University, New Haven, CT, USA., Lapey A; Massachusetts General Hospital, Boston, MA, USA., Mall MA; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité - Universitätsmedizin Berlin, Berlin, Germany; German Center for Lung Research (DZL), associated partner site, Berlin, Germany; German Center for Child and Adolescent Health (DZKJ), partner site Berlin, Berlin, Germany; Cluster of Excellence ImmunoPreCept, Charité - Universitätsmedizin Berlin, Berlin, Germany., McKone EF; St Vincent's University Hospital, Dublin, Ireland., Peckham D; St James's University Hospital, Leeds, UK., Proesmans M; University Hospital of Leuven, Leuven, Belgium., Ramsey B; Seattle Children's Hospital, Seattle, WA, USA., Santamaria SV; Hospital Ramón y Cajal, Madrid, Spain., Smith D; The Prince Charles Hospital, Brisbane, Queensland, Australia., Taylor-Cousar JL; National Jewish Health, Denver, CO, USA., Tullis E; St Michael's Hospital, Toronto, Ontario, Canada., De Wachter E; Universitair Ziekenhuis Brussel, Vrije Universiteit Brussel, Brussels, Belgium., Withers N; Royal Devon United Hospital NHS Foundation Trust, Exeter, UK., Ahluwalia N; Vertex Pharmaceuticals Incorporated, Boston, MA, USA., Conner S; Vertex Pharmaceuticals Incorporated, Boston, MA, USA., Jennings M; Vertex Pharmaceuticals Incorporated, Boston, MA, USA., Lou Y; Vertex Pharmaceuticals Incorporated, Boston, MA, USA., Weinstock TG; Vertex Pharmaceuticals Incorporated, Boston, MA, USA., Keating D; Alfred Health, and Monash University, Melbourne, Victoria, Australia.
Source: Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society [J Cyst Fibros] 2026 Mar 31. Date of Electronic Publication: 2026 Mar 31.
Publication Type: Journal Article
Journal Info: Publisher: Elsevier Country of Publication: Netherlands NLM ID: 101128966 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1873-5010 (Electronic) Linking ISSN: 15691993 NLM ISO Abbreviation: J Cyst Fibros Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:1873-5010
DOI:10.1016/j.jcf.2026.03.016