Lenalidomide-Dexamethasone as an Effective and Well-Tolerated Treatment Option for Refractory Rosai-Dorfman-Destombes Disease: A Clinical and Pharmacophenomic Study.
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| Title: | Lenalidomide-Dexamethasone as an Effective and Well-Tolerated Treatment Option for Refractory Rosai-Dorfman-Destombes Disease: A Clinical and Pharmacophenomic Study. |
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| Authors: | Leung E; Department of Medicine, University of British Columbia, Vancouver, British Columbia, Canada.; Coastal Program for Rare Inflammatory Diseases, Nova Scotia Health Innovation Hub, Halifax, Nova Scotia, Canada., Fragola NR; Every Cure, Philadelphia, Pennsylvania, USA., Sharp EW; Every Cure, Philadelphia, Pennsylvania, USA., Harrison RA; Division of Neurology, University of British Columbia, Vancouver, British Columbia, Canada.; Division of Medical Oncology, BC Cancer, Vancouver, British Columbia, Canada., Peterson E; Division of Hematology, University of British Columbia, Vancouver, British Columbia, Canada., Varghese J; Division of Hematology, University of British Columbia, Vancouver, British Columbia, Canada., Jackson S; Division of Hematology, University of British Columbia, Vancouver, British Columbia, Canada., You XJ; Division of Hematology, McGill University, Montreal, Quebec, Canada., VanderVeer E; Division of Hematology, British Columbia Cancer Agency, Surrey, British Columbia, Canada., Trinder M; Department of Pathology and Laboratory Medicine, University of British Columbia, Vancouver, British Columbia, Canada., Sutherland A; Division of Dermatology, Dalhousie University, Halifax, Nova Scotia, Canada., Dutz J; Department of Dermatology and Skin Sciences, University of British Columbia, Vancouver, British Columbia, Canada., Kaniewski P; Every Cure, Philadelphia, Pennsylvania, USA., McClain KL; Baylor College of Medicine, Texas Children's Cancer and Hematology Centers, Houston, Texas, USA., Abla O; Division of Hematology/Oncology, Department of Pediatrics, The Hospital for Sick Children, Toronto, Ontario, Canada., Fajgenbaum DC; Every Cure, Philadelphia, Pennsylvania, USA.; Division of Translational Medicine & Human Genetics, University of Pennsylvania, Philadelphia, Pennsylvania, USA., Chen LYC; Coastal Program for Rare Inflammatory Diseases, Nova Scotia Health Innovation Hub, Halifax, Nova Scotia, Canada.; Division of Hematology, University of British Columbia, Vancouver, British Columbia, Canada.; Division of Hematology, Dalhousie University, Halifax, Nova Scotia, Canada. |
| Source: | American journal of hematology [Am J Hematol] 2026 Jul; Vol. 101 (7), pp. 1478-1483. Date of Electronic Publication: 2026 Apr 02. |
| Publication Type: | Journal Article; Letter |
| Journal Info: | Publisher: Wiley-Blackwell Country of Publication: United States NLM ID: 7610369 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1096-8652 (Electronic) Linking ISSN: 03618609 NLM ISO Abbreviation: Am J Hematol Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Text: Availability: 0 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 41928050 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Lenalidomide-Dexamethasone as an Effective and Well-Tolerated Treatment Option for Refractory Rosai-Dorfman-Destombes Disease: A Clinical and Pharmacophenomic Study. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Leung+E%22">Leung E</searchLink>; Department of Medicine, University of British Columbia, Vancouver, British Columbia, Canada.; Coastal Program for Rare Inflammatory Diseases, Nova Scotia Health Innovation Hub, Halifax, Nova Scotia, Canada.<br /><searchLink fieldCode="AU" term="%22Fragola+NR%22">Fragola NR</searchLink>; Every Cure, Philadelphia, Pennsylvania, USA.<br /><searchLink fieldCode="AU" term="%22Sharp+EW%22">Sharp EW</searchLink>; Every Cure, Philadelphia, Pennsylvania, USA.<br /><searchLink fieldCode="AU" term="%22Harrison+RA%22">Harrison RA</searchLink>; Division of Neurology, University of British Columbia, Vancouver, British Columbia, Canada.; Division of Medical Oncology, BC Cancer, Vancouver, British Columbia, Canada.<br /><searchLink fieldCode="AU" term="%22Peterson+E%22">Peterson E</searchLink>; Division of Hematology, University of British Columbia, Vancouver, British Columbia, Canada.<br /><searchLink fieldCode="AU" term="%22Varghese+J%22">Varghese J</searchLink>; Division of Hematology, University of British Columbia, Vancouver, British Columbia, Canada.<br /><searchLink fieldCode="AU" term="%22Jackson+S%22">Jackson S</searchLink>; Division of Hematology, University of British Columbia, Vancouver, British Columbia, Canada.<br /><searchLink fieldCode="AU" term="%22You+XJ%22">You XJ</searchLink>; Division of Hematology, McGill University, Montreal, Quebec, Canada.<br /><searchLink fieldCode="AU" term="%22VanderVeer+E%22">VanderVeer E</searchLink>; Division of Hematology, British Columbia Cancer Agency, Surrey, British Columbia, Canada.<br /><searchLink fieldCode="AU" term="%22Trinder+M%22">Trinder M</searchLink>; Department of Pathology and Laboratory Medicine, University of British Columbia, Vancouver, British Columbia, Canada.<br /><searchLink fieldCode="AU" term="%22Sutherland+A%22">Sutherland A</searchLink>; Division of Dermatology, Dalhousie University, Halifax, Nova Scotia, Canada.<br /><searchLink fieldCode="AU" term="%22Dutz+J%22">Dutz J</searchLink>; Department of Dermatology and Skin Sciences, University of British Columbia, Vancouver, British Columbia, Canada.<br /><searchLink fieldCode="AU" term="%22Kaniewski+P%22">Kaniewski P</searchLink>; Every Cure, Philadelphia, Pennsylvania, USA.<br /><searchLink fieldCode="AU" term="%22McClain+KL%22">McClain KL</searchLink>; Baylor College of Medicine, Texas Children's Cancer and Hematology Centers, Houston, Texas, USA.<br /><searchLink fieldCode="AU" term="%22Abla+O%22">Abla O</searchLink>; Division of Hematology/Oncology, Department of Pediatrics, The Hospital for Sick Children, Toronto, Ontario, Canada.<br /><searchLink fieldCode="AU" term="%22Fajgenbaum+DC%22">Fajgenbaum DC</searchLink>; Every Cure, Philadelphia, Pennsylvania, USA.; Division of Translational Medicine & Human Genetics, University of Pennsylvania, Philadelphia, Pennsylvania, USA.<br /><searchLink fieldCode="AU" term="%22Chen+LYC%22">Chen LYC</searchLink>; Coastal Program for Rare Inflammatory Diseases, Nova Scotia Health Innovation Hub, Halifax, Nova Scotia, Canada.; Division of Hematology, University of British Columbia, Vancouver, British Columbia, Canada.; Division of Hematology, Dalhousie University, Halifax, Nova Scotia, Canada. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%227610369%22">American journal of hematology</searchLink> [Am J Hematol] 2026 Jul; Vol. 101 (7), pp. 1478-1483. <i>Date of Electronic Publication: </i>2026 Apr 02. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article; Letter – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Wiley-Blackwell%22">Wiley-Blackwell </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>7610369 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1096-8652 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2203618609%22">03618609 </searchLink><i>NLM ISO Abbreviation: </i>Am J Hematol <i>Subsets: </i>MEDLINE |
| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=41928050 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1002/ajh.70309 Languages: – Code: eng Text: English PhysicalDescription: Pagination: StartPage: 1478 Titles: – TitleFull: Lenalidomide-Dexamethasone as an Effective and Well-Tolerated Treatment Option for Refractory Rosai-Dorfman-Destombes Disease: A Clinical and Pharmacophenomic Study. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Leung E – PersonEntity: Name: NameFull: Fragola NR – PersonEntity: Name: NameFull: Sharp EW – PersonEntity: Name: NameFull: Harrison RA – PersonEntity: Name: NameFull: Peterson E – PersonEntity: Name: NameFull: Varghese J – PersonEntity: Name: NameFull: Jackson S – PersonEntity: Name: NameFull: You XJ – PersonEntity: Name: NameFull: VanderVeer E – PersonEntity: Name: NameFull: Trinder M – PersonEntity: Name: NameFull: Sutherland A – PersonEntity: Name: NameFull: Dutz J – PersonEntity: Name: NameFull: Kaniewski P – PersonEntity: Name: NameFull: McClain KL – PersonEntity: Name: NameFull: Abla O – PersonEntity: Name: NameFull: Fajgenbaum DC – PersonEntity: Name: NameFull: Chen LYC IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 07 Text: 2026 Jul Type: published Y: 2026 Identifiers: – Type: issn-electronic Value: 1096-8652 Numbering: – Type: volume Value: 101 – Type: issue Value: 7 Titles: – TitleFull: American journal of hematology Type: main |
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