Kidney Transplant Outcomes in Coatomer Protein Complex Subunit Alpha (COPA) Syndrome: Report of Five Patients.

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Title: Kidney Transplant Outcomes in Coatomer Protein Complex Subunit Alpha (COPA) Syndrome: Report of Five Patients.
Authors: Triaille C; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Pôle de Pathologies Rhumatismales Systémiques et Inflammatoires (RUMA), Institut de Recherche Expérimentale et Clinique (IREC), Université Catholique de Louvain, Brussels, Belgium. Electronic address: clement.triaille@uclouvain.be., Côté K; Pathology Division, CHU Sainte-Justine, Department of Pediatrics, University of Montreal, Montreal, Canada., Coulombe J; Dermatology, Department of Pediatric, CHU Sainte-Justine, Université de Montréal, Montreal, Canada., Daroux M; Department of Nephrology, Duchenne Hospital, Boulogne-Sur-Mer, France., David C; Département de Médecine Interne, Hôpital Bichat, Assistance Publique Hôpitaux de Paris, Paris, France; Laboratory of Neurogenetics and Neuroinflammation, Imagine Institute, Inserm U1163, Paris, France; COPA study group., Frémond ML; Laboratory of Neurogenetics and Neuroinflammation, Imagine Institute, Inserm U1163, Paris, France; COPA study group; Paediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital, APHP Centre, Université Paris-Cité, Paris, and Reference Centre for Inflammatory Rheumatism, Autoimmune Diseases and Systemic Interferonopathies in Children (RAISE), France., Haddad E; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Department of Pediatrics, Department of Microbiology, Immunology and Infectious Diseases, CHU Sainte-Justine Azrieli Research Center, Université de Montréal, Montreal, Canada., Khan N; Medical City Transplant, Dallas Renal Group, Dallas, Texas., Kokta V; Pathology Division, CHU Sainte-Justine, Department of Pediatrics, University of Montreal, Montreal, Canada., Lapeyraque AL; Pediatric Nephrology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada., Lebas C; Department of Nephrology, CHU de Lille, Lille, France., Matoses Ruipérez ML; Section of Pediatric Rheumatology, Hospital Universitario y Politécnico la Fe, Valencia, Spain., López Montesinos B; Pediatric Rheumatology Unit, Hospital Universitario y Policlínico La Fe, La Fe Health Research Institute, Valencia, Spain., Reumaux H; Pediatric Rheumatology, Jeanne de Flandre Hospital, CHU Lille, Lille, France., Vogel TP; Division of Rheumatology, Department of Pediatrics, Baylor College of Medicine, Houston, Texas; Center for Human Immunobiology, Texas Children's Hospital, Houston, Texas., Morin MP; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada., Phan V; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Pediatric Nephrology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada.
Source: American journal of kidney diseases : the official journal of the National Kidney Foundation [Am J Kidney Dis] 2026 Jul; Vol. 88 (1), pp. 170-176. Date of Electronic Publication: 2026 Apr 01.
Publication Type: Case Reports; Journal Article
Journal Info: Publisher: W.B. Saunders Country of Publication: United States NLM ID: 8110075 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1523-6838 (Electronic) Linking ISSN: 02726386 NLM ISO Abbreviation: Am J Kidney Dis Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:1523-6838
DOI:10.1053/j.ajkd.2025.12.007