Kidney Transplant Outcomes in Coatomer Protein Complex Subunit Alpha (COPA) Syndrome: Report of Five Patients.

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Title: Kidney Transplant Outcomes in Coatomer Protein Complex Subunit Alpha (COPA) Syndrome: Report of Five Patients.
Authors: Triaille C; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Pôle de Pathologies Rhumatismales Systémiques et Inflammatoires (RUMA), Institut de Recherche Expérimentale et Clinique (IREC), Université Catholique de Louvain, Brussels, Belgium. Electronic address: clement.triaille@uclouvain.be., Côté K; Pathology Division, CHU Sainte-Justine, Department of Pediatrics, University of Montreal, Montreal, Canada., Coulombe J; Dermatology, Department of Pediatric, CHU Sainte-Justine, Université de Montréal, Montreal, Canada., Daroux M; Department of Nephrology, Duchenne Hospital, Boulogne-Sur-Mer, France., David C; Département de Médecine Interne, Hôpital Bichat, Assistance Publique Hôpitaux de Paris, Paris, France; Laboratory of Neurogenetics and Neuroinflammation, Imagine Institute, Inserm U1163, Paris, France; COPA study group., Frémond ML; Laboratory of Neurogenetics and Neuroinflammation, Imagine Institute, Inserm U1163, Paris, France; COPA study group; Paediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital, APHP Centre, Université Paris-Cité, Paris, and Reference Centre for Inflammatory Rheumatism, Autoimmune Diseases and Systemic Interferonopathies in Children (RAISE), France., Haddad E; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Department of Pediatrics, Department of Microbiology, Immunology and Infectious Diseases, CHU Sainte-Justine Azrieli Research Center, Université de Montréal, Montreal, Canada., Khan N; Medical City Transplant, Dallas Renal Group, Dallas, Texas., Kokta V; Pathology Division, CHU Sainte-Justine, Department of Pediatrics, University of Montreal, Montreal, Canada., Lapeyraque AL; Pediatric Nephrology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada., Lebas C; Department of Nephrology, CHU de Lille, Lille, France., Matoses Ruipérez ML; Section of Pediatric Rheumatology, Hospital Universitario y Politécnico la Fe, Valencia, Spain., López Montesinos B; Pediatric Rheumatology Unit, Hospital Universitario y Policlínico La Fe, La Fe Health Research Institute, Valencia, Spain., Reumaux H; Pediatric Rheumatology, Jeanne de Flandre Hospital, CHU Lille, Lille, France., Vogel TP; Division of Rheumatology, Department of Pediatrics, Baylor College of Medicine, Houston, Texas; Center for Human Immunobiology, Texas Children's Hospital, Houston, Texas., Morin MP; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada., Phan V; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Pediatric Nephrology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada.
Source: American journal of kidney diseases : the official journal of the National Kidney Foundation [Am J Kidney Dis] 2026 Jul; Vol. 88 (1), pp. 170-176. Date of Electronic Publication: 2026 Apr 01.
Publication Type: Case Reports; Journal Article
Journal Info: Publisher: W.B. Saunders Country of Publication: United States NLM ID: 8110075 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1523-6838 (Electronic) Linking ISSN: 02726386 NLM ISO Abbreviation: Am J Kidney Dis Subsets: MEDLINE
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  Data: Kidney Transplant Outcomes in Coatomer Protein Complex Subunit Alpha (COPA) Syndrome: Report of Five Patients.
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  Data: <searchLink fieldCode="AU" term="%22Triaille+C%22">Triaille C</searchLink>; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Pôle de Pathologies Rhumatismales Systémiques et Inflammatoires (RUMA), Institut de Recherche Expérimentale et Clinique (IREC), Université Catholique de Louvain, Brussels, Belgium. Electronic address: clement.triaille@uclouvain.be.<br /><searchLink fieldCode="AU" term="%22Côté+K%22">Côté K</searchLink>; Pathology Division, CHU Sainte-Justine, Department of Pediatrics, University of Montreal, Montreal, Canada.<br /><searchLink fieldCode="AU" term="%22Coulombe+J%22">Coulombe J</searchLink>; Dermatology, Department of Pediatric, CHU Sainte-Justine, Université de Montréal, Montreal, Canada.<br /><searchLink fieldCode="AU" term="%22Daroux+M%22">Daroux M</searchLink>; Department of Nephrology, Duchenne Hospital, Boulogne-Sur-Mer, France.<br /><searchLink fieldCode="AU" term="%22David+C%22">David C</searchLink>; Département de Médecine Interne, Hôpital Bichat, Assistance Publique Hôpitaux de Paris, Paris, France; Laboratory of Neurogenetics and Neuroinflammation, Imagine Institute, Inserm U1163, Paris, France; COPA study group.<br /><searchLink fieldCode="AU" term="%22Frémond+ML%22">Frémond ML</searchLink>; Laboratory of Neurogenetics and Neuroinflammation, Imagine Institute, Inserm U1163, Paris, France; COPA study group; Paediatric Immunology-Hematology and Rheumatology Unit, Necker Hospital, APHP Centre, Université Paris-Cité, Paris, and Reference Centre for Inflammatory Rheumatism, Autoimmune Diseases and Systemic Interferonopathies in Children (RAISE), France.<br /><searchLink fieldCode="AU" term="%22Haddad+E%22">Haddad E</searchLink>; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Department of Pediatrics, Department of Microbiology, Immunology and Infectious Diseases, CHU Sainte-Justine Azrieli Research Center, Université de Montréal, Montreal, Canada.<br /><searchLink fieldCode="AU" term="%22Khan+N%22">Khan N</searchLink>; Medical City Transplant, Dallas Renal Group, Dallas, Texas.<br /><searchLink fieldCode="AU" term="%22Kokta+V%22">Kokta V</searchLink>; Pathology Division, CHU Sainte-Justine, Department of Pediatrics, University of Montreal, Montreal, Canada.<br /><searchLink fieldCode="AU" term="%22Lapeyraque+AL%22">Lapeyraque AL</searchLink>; Pediatric Nephrology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada.<br /><searchLink fieldCode="AU" term="%22Lebas+C%22">Lebas C</searchLink>; Department of Nephrology, CHU de Lille, Lille, France.<br /><searchLink fieldCode="AU" term="%22Matoses+Ruipérez+ML%22">Matoses Ruipérez ML</searchLink>; Section of Pediatric Rheumatology, Hospital Universitario y Politécnico la Fe, Valencia, Spain.<br /><searchLink fieldCode="AU" term="%22López+Montesinos+B%22">López Montesinos B</searchLink>; Pediatric Rheumatology Unit, Hospital Universitario y Policlínico La Fe, La Fe Health Research Institute, Valencia, Spain.<br /><searchLink fieldCode="AU" term="%22Reumaux+H%22">Reumaux H</searchLink>; Pediatric Rheumatology, Jeanne de Flandre Hospital, CHU Lille, Lille, France.<br /><searchLink fieldCode="AU" term="%22Vogel+TP%22">Vogel TP</searchLink>; Division of Rheumatology, Department of Pediatrics, Baylor College of Medicine, Houston, Texas; Center for Human Immunobiology, Texas Children's Hospital, Houston, Texas.<br /><searchLink fieldCode="AU" term="%22Morin+MP%22">Morin MP</searchLink>; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada.<br /><searchLink fieldCode="AU" term="%22Phan+V%22">Phan V</searchLink>; Pediatric Rheumatology and Immunology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada; Pediatric Nephrology, Department of Pediatrics, CHU Sainte-Justine, Université de Montréal, Montreal, Canada.
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  Data: <searchLink fieldCode="JN" term="%228110075%22">American journal of kidney diseases : the official journal of the National Kidney Foundation</searchLink> [Am J Kidney Dis] 2026 Jul; Vol. 88 (1), pp. 170-176. <i>Date of Electronic Publication: </i>2026 Apr 01.
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22W%2EB%2E+Saunders%22">W.B. Saunders </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>8110075 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1523-6838 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2202726386%22">02726386 </searchLink><i>NLM ISO Abbreviation: </i>Am J Kidney Dis <i>Subsets: </i>MEDLINE
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