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Restoration of lysosomal membrane integrity in cell models of Pompe disease depends on fatty acid synthase and its product palmitic acid.

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Title: Restoration of lysosomal membrane integrity in cell models of Pompe disease depends on fatty acid synthase and its product palmitic acid.
Authors: Le Guillou E; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France.; Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, 75015, France., Segaloni A; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France., Gadault A; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France., Oliveira Dias C; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France., Henneman NF; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France., Su M; Institute of Pharmaceutical Sciences, Pharmaceutical (Bio-)Analysis, University of Tübingen, Auf Der Morgenstelle 8, Tübingen, 72076, Germany., Nemazanyy I; Platform for Metabolic Analyses, Structure Fédérative de Recherche Necker, INSERM US24/CNRS UAR 3633, Paris, 75015, France., Hifdi N; Institute of Cardiovascular and Metabolic Diseases (I2MC), INSERM-UMR 1297, University Paul Sabatier, Toulouse, France., Nivet-Antoine V; Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, 75015, France., Laemmerhofer M; Institute of Pharmaceutical Sciences, Pharmaceutical (Bio-)Analysis, University of Tübingen, Auf Der Morgenstelle 8, Tübingen, 72076, Germany., Hnia K; Institute of Cardiovascular and Metabolic Diseases (I2MC), INSERM-UMR 1297, University Paul Sabatier, Toulouse, France., Caillaud C; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France.; Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, 75015, France., Panasyuk G; Institut Necker-Enfants Malades (INEM), Paris, 75015, France. ganna.panasyuk@inserm.fr.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France. ganna.panasyuk@inserm.fr.; Université Paris Cité, Paris, 75006, France. ganna.panasyuk@inserm.fr.
Source: Cellular & molecular biology letters [Cell Mol Biol Lett] 2026 Apr 09; Vol. 31 (1). Date of Electronic Publication: 2026 Apr 09.
Publication Type: Journal Article
Journal Info: Publisher: BioMed Central Country of Publication: England NLM ID: 9607427 Publication Model: Electronic Cited Medium: Internet ISSN: 1689-1392 (Electronic) Linking ISSN: 14258153 NLM ISO Abbreviation: Cell Mol Biol Lett Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Restoration of lysosomal membrane integrity in cell models of Pompe disease depends on fatty acid synthase and its product palmitic acid.
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  Data: <searchLink fieldCode="AU" term="%22Le+Guillou+E%22">Le Guillou E</searchLink>; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France.; Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, 75015, France.<br /><searchLink fieldCode="AU" term="%22Segaloni+A%22">Segaloni A</searchLink>; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France.<br /><searchLink fieldCode="AU" term="%22Gadault+A%22">Gadault A</searchLink>; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France.<br /><searchLink fieldCode="AU" term="%22Oliveira+Dias+C%22">Oliveira Dias C</searchLink>; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France.<br /><searchLink fieldCode="AU" term="%22Henneman+NF%22">Henneman NF</searchLink>; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France.<br /><searchLink fieldCode="AU" term="%22Su+M%22">Su M</searchLink>; Institute of Pharmaceutical Sciences, Pharmaceutical (Bio-)Analysis, University of Tübingen, Auf Der Morgenstelle 8, Tübingen, 72076, Germany.<br /><searchLink fieldCode="AU" term="%22Nemazanyy+I%22">Nemazanyy I</searchLink>; Platform for Metabolic Analyses, Structure Fédérative de Recherche Necker, INSERM US24/CNRS UAR 3633, Paris, 75015, France.<br /><searchLink fieldCode="AU" term="%22Hifdi+N%22">Hifdi N</searchLink>; Institute of Cardiovascular and Metabolic Diseases (I2MC), INSERM-UMR 1297, University Paul Sabatier, Toulouse, France.<br /><searchLink fieldCode="AU" term="%22Nivet-Antoine+V%22">Nivet-Antoine V</searchLink>; Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, 75015, France.<br /><searchLink fieldCode="AU" term="%22Laemmerhofer+M%22">Laemmerhofer M</searchLink>; Institute of Pharmaceutical Sciences, Pharmaceutical (Bio-)Analysis, University of Tübingen, Auf Der Morgenstelle 8, Tübingen, 72076, Germany.<br /><searchLink fieldCode="AU" term="%22Hnia+K%22">Hnia K</searchLink>; Institute of Cardiovascular and Metabolic Diseases (I2MC), INSERM-UMR 1297, University Paul Sabatier, Toulouse, France.<br /><searchLink fieldCode="AU" term="%22Caillaud+C%22">Caillaud C</searchLink>; Institut Necker-Enfants Malades (INEM), Paris, 75015, France.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France.; Université Paris Cité, Paris, 75006, France.; Biochemistry Laboratory, Necker-Enfants Malades Hospital, APHP, Paris, 75015, France.<br /><searchLink fieldCode="AU" term="%22Panasyuk+G%22">Panasyuk G</searchLink>; Institut Necker-Enfants Malades (INEM), Paris, 75015, France. ganna.panasyuk@inserm.fr.; INSERM U1151/CNRS UMR 8253, Paris, 75015, France. ganna.panasyuk@inserm.fr.; Université Paris Cité, Paris, 75006, France. ganna.panasyuk@inserm.fr.
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  Data: <searchLink fieldCode="JN" term="%229607427%22">Cellular & molecular biology letters</searchLink> [Cell Mol Biol Lett] 2026 Apr 09; Vol. 31 (1). <i>Date of Electronic Publication: </i>2026 Apr 09.
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