Long-term restoration of auditory function in a DFNA2 mouse model by adenine base editing.

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Title: Long-term restoration of auditory function in a DFNA2 mouse model by adenine base editing.
Authors: Kong Y; Department of Otorhinolaryngology-Head & Neck Surgery, West China Hospital, Sichuan University, Chengdu, 610041, China.; Institute of Rare Diseases, West China Hospital, Sichuan University, Chengdu, 610000, China., Zhang Y; Department of Otorhinolaryngology-Head & Neck Surgery, West China Hospital, Sichuan University, Chengdu, 610041, China. yingjiezhang@scu.edu.cn.; Institute of Rare Diseases, West China Hospital, Sichuan University, Chengdu, 610000, China. yingjiezhang@scu.edu.cn., Xie E; Department of Otorhinolaryngology-Head & Neck Surgery, West China Hospital, Sichuan University, Chengdu, 610041, China., Li X; Department of Otorhinolaryngology-Head & Neck Surgery, West China Hospital, Sichuan University, Chengdu, 610041, China.; Institute of Rare Diseases, West China Hospital, Sichuan University, Chengdu, 610000, China., Peng Z; Institute of Rare Diseases, West China Hospital, Sichuan University, Chengdu, 610000, China., Zhang J; Institute of Rare Diseases, West China Hospital, Sichuan University, Chengdu, 610000, China., Zhao Y; Department of Otorhinolaryngology-Head & Neck Surgery, West China Hospital, Sichuan University, Chengdu, 610041, China. yuzhao@wchscu.edu.cn., Yuan H; Department of Otorhinolaryngology-Head & Neck Surgery, West China Hospital, Sichuan University, Chengdu, 610041, China. yuanhj301@wchscu.cn.; Institute of Rare Diseases, West China Hospital, Sichuan University, Chengdu, 610000, China. yuanhj301@wchscu.cn.
Source: EMBO molecular medicine [EMBO Mol Med] 2026 Jun; Vol. 18 (6), pp. 2293-2321. Date of Electronic Publication: 2026 May 20.
Publication Type: Journal Article
Journal Info: Publisher: EMBO Press Country of Publication: Germany NLM ID: 101487380 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1757-4684 (Electronic) Linking ISSN: 17574676 NLM ISO Abbreviation: EMBO Mol Med Subsets: MEDLINE
Database: MEDLINE Ultimate
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ISSN:1757-4684
DOI:10.1038/s44321-026-00433-5