Longitudinal Assessment of Muscle Involvement in Late-Onset Pompe Disease Using Quantitative MRI: A Prospective Cohort Study.

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Title: Longitudinal Assessment of Muscle Involvement in Late-Onset Pompe Disease Using Quantitative MRI: A Prospective Cohort Study.
Authors: De Lorenzo A; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Forsting J; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Froeling M; Department of Radiology, University Medical Centre Utrecht, Utrecht, the Netherlands., Güttsches AK; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Enax-Krumova E; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Kleefeld F; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Öztürk M; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Knieling F; Department of Pediatrics and Adolescent Medicine, University Hospital Erlangen, Friedrich-Alexander-Universität (FAU) Erlangen-Nürnberg, Erlangen, Germany.; Translational Pediatrics, Department of Pediatrics and Adolescent Medicine, University Hospital Erlangen, Friedrich-Alexander-Universität (FAU) Erlangen-Nürnberg, Erlangen, Germany., Vorgerd M; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Rehmann R; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Ruck T; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany., Schlaffke L; Department of Neurology, BG-University Hospital Bergmannsheil, Ruhr-University Bochum, Bochum, Germany.; Heimer Institute for Muscle Research, BG-University Hospital Bergmannsheil, Bochum, Germany.; Department of Neuropediatrics and Social Pediatrics, University Hospital of Pediatrics and Adolescent Medicine, St. Josef-Hospital, Ruhr-University Bochum, Bochum, Germany.; Department of Information Technology, Dortmund University of Applied Sciences and Arts, Dortmund, Germany.
Source: Journal of cachexia, sarcopenia and muscle [J Cachexia Sarcopenia Muscle] 2026 Jun; Vol. 17 (3), pp. e70304.
Publication Type: Journal Article
Journal Info: Publisher: John Wiley & Sons Ltd on behalf of Society on Sarcopenia, Cachexia and Wasting Disorders Country of Publication: Germany NLM ID: 101552883 Publication Model: Print Cited Medium: Internet ISSN: 2190-6009 (Electronic) Linking ISSN: 21905991 NLM ISO Abbreviation: J Cachexia Sarcopenia Muscle Subsets: MEDLINE
Database: MEDLINE Ultimate
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ISSN:2190-6009
DOI:10.1002/jcsm.70304