View in EDS

Extracellular matrix deposition drives disease progression and reduces rapamycin response in lymphangioleiomyomatosis.

Saved in:
Bibliographic Details
Title: Extracellular matrix deposition drives disease progression and reduces rapamycin response in lymphangioleiomyomatosis.
Authors: Clements D; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK debbie.clements@nottingham.ac.uk., Babaei-Jadidi R; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK., Johnson J; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK., Miller S; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK., Shah N; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK., Sand JMB; Nordic Bioscience A/S, Herlev, Denmark., Leeming DJ; Nordic Bioscience A/S, Herlev, Denmark., Borthwick LA; Biosciences Institute, Newcastle University, Newcastle upon Tyne, UK., Fisher AJ; Institute of Transplantation, Freeman Hospital, Newcastle upon Tyne, UK.; Newcastle University Translational and Clinical Research Institute, Newcastle Upon Tyne, UK., Dufour A; Department of Physiology and Pharmacology, University of Calgary, Calgary, AB, Canada., Johnson SR; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK.; National Centre for Lymphangioleiomyomatosis, Nottingham University Hospitals NHS Trust, Nottingham, UK.
Source: The European respiratory journal [Eur Respir J] 2026 May 21; Vol. 67 (5). Date of Electronic Publication: 2026 May 21 (Print Publication: 2026).
Publication Type: Journal Article
Journal Info: Publisher: European Respiratory Society Country of Publication: England NLM ID: 8803460 Publication Model: Electronic-Print Cited Medium: Internet ISSN: 1399-3003 (Electronic) Linking ISSN: 09031936 NLM ISO Abbreviation: Eur Respir J Subsets: MEDLINE
Database: MEDLINE Ultimate
FullText Text:
  Availability: 0
Header DbId: mdl
DbLabel: MEDLINE Ultimate
An: 41381226
AccessLevel: 2
PubType: Academic Journal
PubTypeId: academicJournal
PreciseRelevancyScore: 0
IllustrationInfo
Items – Name: Title
  Label: Title
  Group: Ti
  Data: Extracellular matrix deposition drives disease progression and reduces rapamycin response in lymphangioleiomyomatosis.
– Name: Author
  Label: Authors
  Group: Au
  Data: <searchLink fieldCode="AU" term="%22Clements+D%22">Clements D</searchLink>; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK debbie.clements@nottingham.ac.uk.<br /><searchLink fieldCode="AU" term="%22Babaei-Jadidi+R%22">Babaei-Jadidi R</searchLink>; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK.<br /><searchLink fieldCode="AU" term="%22Johnson+J%22">Johnson J</searchLink>; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK.<br /><searchLink fieldCode="AU" term="%22Miller+S%22">Miller S</searchLink>; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK.<br /><searchLink fieldCode="AU" term="%22Shah+N%22">Shah N</searchLink>; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK.<br /><searchLink fieldCode="AU" term="%22Sand+JMB%22">Sand JMB</searchLink>; Nordic Bioscience A/S, Herlev, Denmark.<br /><searchLink fieldCode="AU" term="%22Leeming+DJ%22">Leeming DJ</searchLink>; Nordic Bioscience A/S, Herlev, Denmark.<br /><searchLink fieldCode="AU" term="%22Borthwick+LA%22">Borthwick LA</searchLink>; Biosciences Institute, Newcastle University, Newcastle upon Tyne, UK.<br /><searchLink fieldCode="AU" term="%22Fisher+AJ%22">Fisher AJ</searchLink>; Institute of Transplantation, Freeman Hospital, Newcastle upon Tyne, UK.; Newcastle University Translational and Clinical Research Institute, Newcastle Upon Tyne, UK.<br /><searchLink fieldCode="AU" term="%22Dufour+A%22">Dufour A</searchLink>; Department of Physiology and Pharmacology, University of Calgary, Calgary, AB, Canada.<br /><searchLink fieldCode="AU" term="%22Johnson+SR%22">Johnson SR</searchLink>; Centre for Respiratory Research, NIHR Nottingham Biomedical Research Centre and Biodiscovery Institute, University of Nottingham, Nottingham, UK.; National Centre for Lymphangioleiomyomatosis, Nottingham University Hospitals NHS Trust, Nottingham, UK.
– Name: TitleSource
  Label: Source
  Group: Src
  Data: <searchLink fieldCode="JN" term="%228803460%22">The European respiratory journal</searchLink> [Eur Respir J] 2026 May 21; Vol. 67 (5). <i>Date of Electronic Publication: </i>2026 May 21 (<i>Print Publication: </i>2026).
– Name: TypePub
  Label: Publication Type
  Group: TypPub
  Data: Journal Article
– Name: TitleSource
  Label: Journal Info
  Group: Src
  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22European+Respiratory+Society%22">European Respiratory Society </searchLink><i>Country of Publication: </i>England <i>NLM ID: </i>8803460 <i>Publication Model: </i>Electronic-Print <i>Cited Medium: </i>Internet <i>ISSN: </i>1399-3003 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2209031936%22">09031936 </searchLink><i>NLM ISO Abbreviation: </i>Eur Respir J <i>Subsets: </i>MEDLINE
PLink https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=41381226
RecordInfo BibRecord:
  BibEntity:
    Identifiers:
      – Type: doi
        Value: 10.1183/13993003.00492-2025
    Languages:
      – Code: eng
        Text: English
    Titles:
      – TitleFull: Extracellular matrix deposition drives disease progression and reduces rapamycin response in lymphangioleiomyomatosis.
        Type: main
  BibRelationships:
    HasContributorRelationships:
      – PersonEntity:
          Name:
            NameFull: Clements D
      – PersonEntity:
          Name:
            NameFull: Babaei-Jadidi R
      – PersonEntity:
          Name:
            NameFull: Johnson J
      – PersonEntity:
          Name:
            NameFull: Miller S
      – PersonEntity:
          Name:
            NameFull: Shah N
      – PersonEntity:
          Name:
            NameFull: Sand JMB
      – PersonEntity:
          Name:
            NameFull: Leeming DJ
      – PersonEntity:
          Name:
            NameFull: Borthwick LA
      – PersonEntity:
          Name:
            NameFull: Fisher AJ
      – PersonEntity:
          Name:
            NameFull: Dufour A
      – PersonEntity:
          Name:
            NameFull: Johnson SR
    IsPartOfRelationships:
      – BibEntity:
          Dates:
            – D: 21
              M: 05
              Text: 2026 May 21
              Type: published
              Y: 2026
          Identifiers:
            – Type: issn-electronic
              Value: 1399-3003
          Numbering:
            – Type: volume
              Value: 67
            – Type: issue
              Value: 5
          Titles:
            – TitleFull: The European respiratory journal
              Type: main
ResultId 1